Congenital generalized lipodystrophy: Berardinelli syndrome. Report of two siblings
Two successively born infants with Berardinelli syndrome, an unusual lipodystrophic disease, are reported.In addition to hepatomegaly, accelerated growth, muscle hypertrophy, lack of adipose tissue, bar drain board hirsutism and hypertriglyceridemia, which are the characteristics of the syndrome, these brothers demonstrated bilateral, symmetrical,